Ectopia Cordis: An Uncommon Fatal Disease

نویسندگان

چکیده

The Video can be viewed in the online version of this article [https://dx.doi.org/10.1016/j.athoracsur.2020.12.097] on https://www.annalsthoracicsurgery.org.During a mission Kinshasa Democratic Republic Congo 2019, case ectopia cordis was diagnosed (Video). This amazing video shows newborn opening its eyes with an extrathoracic beating heart.The 1900 g boy born at 33 weeks’ gestation transferred to our unit (Figure 1). Unfortunately, died sixth day before surgical procedure acute hemodynamic failure.The is rare birth defect characterized by location heart outside thorax. Its prevalence 0.1% all defects, and annual incidence estimated between 5.5 7.9 per million live births.1Amato J.A. Zelen J. Talwalkar N.G. Single-stage repair thoracic cordis.Ann Thorac Surg. 1995; 59: 518Abstract Full Text PDF PubMed Scopus (58) Google Scholar It isolated or associated defects.The first anatomical description probably that Niels Stensen, but it Haller we owe term his 1706.2Millhouse R.F. Joos H.A. Extrathoracic cordis: report cases review literature.Am Heart 1959; 57: 470Crossref (16) ScholarEctopia large majority various cardiac malformations, interventricular communication, interatrial tetralogy Fallot. for such very difficult poor results, because there no place inside thorax put into.These uncommon pathologies are seen yet pregnancy monitoring not optimal. https://www.annalsthoracicsurgery.org. During heart. failure. defects. Ectopia into. These Supplementary Datahttps://www.annalsthoracicsurgery.org/cms/asset/043cca10-5da0-44d4-b95a-ea8a7596c1e1/mmc1.mp4Loading ... Download .mp4 (3.23 MB) Help files https://www.annalsthoracicsurgery.org/cms/asset/043cca10-5da0-44d4-b95a-ea8a7596c1e1/mmc1.mp4Loading

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ژورنال

عنوان ژورنال: The Annals of Thoracic Surgery

سال: 2021

ISSN: ['1552-6259', '0003-4975']

DOI: https://doi.org/10.1016/j.athoracsur.2020.12.097